Leber's congenital amaurosis.

rig. renpheralfundus cS. We have had occasion to see a similar case, first in 1974 when the patient, a black female with no apparent vision but otherwise well, was 6 months old. At that time dilated fundus examination under anaesthesia (EUA) was normal. Repeat EUA in 1977 at age 4 years revealed bilateral peripheral fundus lesions essentially identical to those described by Chew et al. (Figs. 1, 2), along with bilaterally unrecordable ERGs and flash VERs. Our case provides further evidence that this fundus variant of Leber's amaurosis develops between 6 months and 2 years of age. Eye Foundation Hospital, H SKALKA University Station, Birmingham, Alabama 35294, USA